A young man with generalised hyperkeratotic papules: a case of Darier's disease
نویسنده
چکیده
Tuen Mun Social Hygiene Clinic, 9/F, Tuen Mun Hospital, Ambulatory Care Centre, Ching Chung Koon Road, Tuen Mun, New Territories, Hong Kong Darier's disease (Keratosis follicularis) is an uncommon autosomal dominant genodermatosis. Patients present with hyperkeratotic papules in seborrhoeic areas with nail abnormalities. We describe a young gentleman with this disorder for more than three years. A brief review of its clinical features and treatment is also made in this report.
منابع مشابه
Localized Darier's disease or Acantholytic Dyskeratotic epidermal nevus: A case report
Patients with keratotic lesions distributed in a unilateral, linear, zosteriform or localized pattern and revealing histopathologic features of dyskeratotic acantholysis have been reported previously. There is some controversy in the appropriate nosologic classification of this entity. Some authors consider it as a localized form of Darier’s disease while others place it as a variant of e...
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Darier's disease, also known as keratosis follicularis or dyskeratosis follicularis, is a rare disorder of keratinization. It is an autosomal dominant genodermatosis with high penetrance and variable expressivity. Its manifestation appears as hyperkeratotic papules primarily affecting seborrheic areas on the head, neck, thorax, and less frequently the oral mucosa. When oral manifestations are p...
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تاریخ انتشار 2003